Background and Purpose: Tetra-amelia is a syndrome characterized by absence (complete) for all four members and anomalies. The objective of this report was to describe the case of a patient with tetra-amelia underwent arthrodesis of spine to correct severe scoliosis. Case report: Male patient, 12 years old, 41.1 kg, carrying tetra-amelia, underwent surgery to correct spine with severe scoliosis spine arthrodesis between T4 and L1. Discussion: The management of the patient with tetra-amelia becomes a challenge for the implications of the airway, intraoperative monitoring, fluid replacement and response to vasoactive drugs. This syndrome is uncommon and rare reports in the literature also.
Thiago Mamôru Sakae and Alexandre Carlos Buffon